See Also: isovaleric acidemia(medicine)
isovaleric acid(medicine)
acidemia(medicine)
2-ketoadipic acidemia(medicine)
fumaric acidemia(medicine)
hyperpipecolic acidemia(medicine)
lactic acidemia(medicine)
methylmalonic acidemia(medicine)
propionic acidemia(medicine)

latimeria (iou) and isovaleric acidemia (medicine)


latimeria (iou)



latimeria noun. M20.
[mod. Latin, from Marjorie E. D. Courtenay-Latimer (b. 1907), S. African museum curator + -IA1.]
Zoology. Any coelacanth of the extant deep-sea genus Latimeria.

isovaleric acidemia (medicine)


isovaleric acidemia


A disorder of leucine metabolism characterised by the excessive production of isovaleric acid upon protein ingestion or during infectious episodes; severe metabolic acidosis results from the large quantities of acid formed; autosomal recessive inheritance; due to a deficiency of isovaleryl-CoA dehydrogenase.

Synonym: sweaty feet syndrome.