See Also: porphyria cutanea tarda hereditaria(medicine)
porphyria cutanea tarda(medicine)
porphyria cutanea tarda symptomatica(medicine)
syphilis hereditaria tarda(medicine)
Herbal medicine (botanical medicine, herbology, phytomedicine)(health)
vena cutanea(medicine)
protocoproporphyria hereditaria(medicine)
sclerosis cutanea(medicine)
syphilis hereditaria(medicine)
adynamia episodica hereditaria(medicine)

porphyria cutanea tarda hereditaria (medicine)


porphyria cutanea tarda hereditaria -->
porphyria cutanea tarda


A form of hepatic porphyria (porphyria, hepatic) characterised by photosensitivity resulting in bullae that rupture easily to form shallow ulcers. This condition occurs in two forms: a sporadic, nonfamilial form that begins in middle age and has normal amounts of uroporphyrinogen decarboxylase with diminished activity in the liver; and a familial form in which there is an autosomal dominant inherited deficiency of uroporphyrinogen decarboxylase in the liver and red blood cells.